Malformasi Anorektal. ANGKA KEBERHASILAN POSTEROSAGITTAL ANORECTOPLASTY (PSARP) YANG DINILAI DARI SKOR KLOTZ PADA PASIEN MALFORMASI ANOREKTAL. Faktor Risiko yang Memengaruhi Luaran Klinis Malformasi Anorektal pada Neonatus di RSUD Dr. Zainoel Abidin, Banda Aceh. Article. Full-text available.

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The repair of an anorectal malformation requires a meticulous and delicate technique and a surgeon with experience in the management of these defects. Operative Management of Anomalies in Male. The length of this common channel can range from 1 to 10 cm. The goals of surgical treatment are to achieve bowel control, urinary control, and normal sexual function. Hydrosoluble contrast material is injected into the distal stoma to demonstrate the precise location of the distal rectum and its likely urinary communication.

Waiting 16—24 hours for enough abdominal distension to demonstrate the presence of a rectoperineal fistula or rectovestibular fistula applies to females as well. Once the diagnosis of the specific defect is established, the functional prognosis can be rapidly predicted, which is vital in order to avoid raising false expectations in the parents.

This study is vital in determining the anatomy so the definitive repair can be planned. The proximal stoma is connected to the upper gastrointestinal tract and drains stool. These complications may compromise the ultimate functional prognosis.

Malformasi Anorektal | Lokananta | Jurnal Kedokteran Meditek

Most of these patients have excellent sphincter mechanisms and a normal sacrum. They can undergo a posterior sagital anoplasty whereas male babies with evidence of a recto-urinary tract communication should undergo fecal diversion with a colostomy.

History Imperforate anus has been a well-known condition since antiquity. If the air column is greater than 1 cm from the perineum, a colostomy is indicated. zdalah

The child shows signs that he is “feeling” while having a bowel movement as he pushes. For these patients, an effective bowel management program, including enema and dietary restrictions has been devised to improve their quality of life.


In cases of rectovestibular fistula, the posterior sagittal incision can be shorter than in male patients with anore,tal fistulae.

The laparoscopically-assisted anorectal approach consists in mobilizing and bringing the rectum through the pelvic floor sphincter muscles through a minimal posterior incision. Early decision-making The early management of a newborn infant born with an anorectal anomaly is crucial and two important questions must be answered during the first 24 to 48 hours of life. An abdominal ultrasound determines the presence of an obstructive uropathy as well as the presence of a hydrocolpos.

Those that survived most likely suffered from a type of defect that would now be recognized as “low”. The main clinical manifestation of this is constipation, which seems to be more severe in patients with lower defects. Such children need supervision to avoid fecal impaction, constipation, and soiling. Both the urinary tract and the distended vagina may need to be dealt with in the newborn period to avoid serious complications.

A definitive repair in the newborn period avoids a colostomy but there is considerable risk to the urinary tract with this practice because the surgeon does not know the precise anorectal defect. OEIS Omphalocele, exstrophy, imperforate anus, and spinal defects.

The repair of patients with a common channel less than three cm is reproducible and is feasible for most pediatric surgeons. Plain radiographs of the spine can show spinal anomalies such as spina bifida and spinal malfor,asi. Colostomy prior to the main repair avoids the complications of infection and dehiscence.

Classification of anorectal malformations — initial approach, diagnostic tests, and colostomy. These findings are associated with a high malformation and therefore a colostomy should be performed. Support Center Support Center. The presence of a megarectum prior to the pull-through does correlate with postoperative constipation. The surgical approach to repairing these defects changed dramatically in with the introduction of the posterior sagittal approach, which allowed surgeons to view the anatomy of these defects clearly, to repair them under direct vision, and to learn about the complex anatomic arrangement of the junction of rectum and genitourinary tract [ 1 – 6 ].


This is because the most distal part of the rectum in these children is surrounded by a funnel-like voluntary muscle structure that keeps that part of the rectum collapsed and empty. For that child, one should not expect him to achieve voluntary bowel control.

Anorectal malformations

Urinary control varies based on the length of the common channel. The patient is seen each day and an x-ray film of the abdomen is taken so that they can be monitored on a daily basis for the amount and location of any stool left in the colon, as well as the presence of stool in anorektsl underwear. Most patients with an anorectal malformation suffer from a disturbance of this sophisticated bowel motility mechanism. In the normal patient, the voluntary muscle structures are represented by the levators, muscle complex, and external sphincter.

Anorectal Malformations in Children. This article has been corrected. A cross-table lateral x-ray should be performed, and will help determine the need for a colostomy. At the time of defecation, the voluntary muscle structures relax.

Anorectal malformations

The anal canal is normal and externally the anus appear normal. Anorectal malformations ARM represent a spectrum of abnormalities ranging from mild anal anomalies to complex cloacal malformations. Performance of a new pull-through operation should be avoided so that the patient’s rectal reservoir is preserved. For patients with cloaca, functional prognosis with regard to achieving fecal continence depends on the complexity of the defect and the status of the spine and sacrum.

The results of treatment are dramatically different, and so we do not group these two defects into the same category [ 7 ]. Increased heritability of certain types of anorectal malformations. The patient may then receive only a colostomy and subsequently may suffer from sepsis, acidosis, and sometimes death.