Langerhans cell histiocytosis: a rare cause of cholestasis in adult patients. Case report. Histiocitosis de Langerhans: causa infrecuente de colestasis en el. a Unidad Médico-Quirúrgica de Enfermedades Respiratorias. Área de Neumopatías Intersticiales y Ocupacionales. Hospital Universitario Virgen del Rocío. Abstract. GOMEZ, ANA MARÍA et al. Langerhans cell histiocytosis in children. A description of 10 cases. CES Med. [online]. , vol, n.2, pp

Author: Mazshura Dazuru
Country: Iceland
Language: English (Spanish)
Genre: History
Published (Last): 27 November 2004
Pages: 279
PDF File Size: 1.34 Mb
ePub File Size: 4.27 Mb
ISBN: 327-3-93859-265-1
Downloads: 45782
Price: Free* [*Free Regsitration Required]
Uploader: Dolrajas

Manuscripts will be submitted electronically using the following web site: It is a monthly Journal that publishes a total of 12 issues, which contain these types of articles to different extents. An ultrastructural study by transmission electron microscopy reveals the presence of Birbeck granules, although the most widely-used technique to reach a diagnosis is immunohistochemistry Langerhans cells are positive for staining with S, DC68 and CD1a.

Bravo 1M.

Pulmonary Langerhans cell histiocytosis: These are, in decreasing frequency: Chest,pp. The symptoms depend on the organ or organs involved. Langerhans cell histiocytosis is a rare histiocitoiss with different clinical and pathological presentation, is clinically divided into three groups: There is no standard therapy in adults due to the low number of existing cases, so treatment will depend on the degree of involvement.


Histiocotosis measures contextual citation impact by wighting citations based on the total number of citations in a subject field. After the diagnosis of Langerhans cell histiocytosis in the skin biopsy, the liver biopsy simple was reviewed and histological sections were taken from the piece of pancreas. Spanish pdf Article in xml format Article references How to cite this article Automatic translation Send this article by e-mail.

Therefore, the submission of manuscripts written in either Spanish or English is welcome. Annals of Pediatrics is the Body of Scientific Expression of the Association and is the vehicle through which members communicate. Relapsing nodular lesions in the course of adult pulmonary Langerhans cell histiocytosis. Subscriber If you already have your login data, please click here.

It gives few symptoms, and it is usually diagnosed in the autopsy 3where fibrosis may prevail over histiocytosic infiltration. Nevertheless, three months later the patient came to our hospital due to persistent analytical cholestasis and weight loss 30 kg since the initial episode histiocitosls acute pancreatitisdespite an adequate intake of calories.

Journal of Hepatology ; Previous article Next article. Show all Show less.

There was a problem providing the content you requested

Clinical outcomes of pulmonary Langerhans’- cell histiocytosis in adults. CiteScore measures average citations received per document published. A description of 10 cases.

Open biopsy for chronic diffuse infiltration lung disease: This item has received. Subscribe to our Newsletter.


The Impact Factor measures the average number of citations received in a particular year by papers published in the journal during the two receding years.

This form of presentation is rare, and seems to be a variant of congenital self-healing reticulohistiocytosis. Cl 10 A- Other types of articles such as reviews, editorials, special articles, clinical reports, and letters to the Editor are also published in the Journal. Liver involvement in Langehan’s re histiocytosis. Liver transplantation in an adult with lxngerhans cholangitis due to Langerhans cell histiocytosis. It was decided to perform a bypass surgery and a hepaticojejunostomy and a gastrojejunostomy were performed.

Gastrointestinal involvement in Langerhans cell histiocytosis. A biopsy of the lesions showed that these lesions were lngerhans with Langerhans cell histiocytosis.

Histiocitosis de células de Langerhans en niños. Descripción de 10 casos

SRJ is a prestige metric based on the idea that not all citations are the same. Vidal Serrano aE. Full text is only aviable in PDF. Of the 10 patients 5 had risk organ involvement and 1 died in the observation period.