English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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Degos disease – Wikidata
Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. Go to the members area of the website of the AEDV, https: Genetic counseling A genetic predisposition with an autosomal dominant trait has been suggested. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field.
CiteScore measures average citations received per document published. Summary and related texts. A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis. Specialised Social Services Eurordis directory. If you are a member of the AEDV: Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal.
Read this article in English. The documents contained in this web site are presented for information purposes only. Subscriber If you already have your login data, please click here. Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed.
For all other comments, please send your remarks via contact us. It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis.
In early stages, histology of lesions may reveal a superficial and deep perivascular lymphocytic infiltration with distinct mucin deposition.
Enfermedad de Degos
Differential diagnosis The histology of early lesions resembles cutaneous lupus erythematosus see this term. The histology of early lesions resembles cutaneous lupus erythematosus see this term. As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory.
Diagnosis is dgos primarily on the cutaneous clinical picture that is nearly pathognomonic. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. Disease definition Malignant atrophic papulosis MAP is deegos rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.
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More developed lesions can imitate deegos sclerosus see this term. Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine dego heparin have achieved a partial regression of skin lesions in some individual cases.
Management and treatment Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. This condition is chronic and lesions persist over years, often throughout life.
Only comments written in English can be processed. Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0. In the year has been indexed in the Medlinedatabase, and has become a vehicle for expressing the most current Spanish medicine and modern.
This item has received. Other search option s Alphabetical list. Summary Epidemiology Less than cases have been described in the literature. SRJ is a prestige metric based on the idea that not all citations are the same.
No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been tested successfully in one case with intestinal and CNS manifestations.
Additional information Further information on this disease Classification s 3 Gene s 0 Clinical signs and symptoms Publications in PubMed Other website s 7. The etiopathogenesis of the disease remains unknown. May Pages ee22 Pages Are you a health professional able to prescribe or dispense drugs? Previous article Next article. Many patients have been reported to have defects in blood coagulation. MAP enfeermedad occurs in adults aged with skin lesions that appear initially dgos small erythematous papules, predominantly on the trunk and the upper extremities.
Over several days, the center of the lesions sinks and develops a characteristic morphology: Pemphigus Vegetans in the Inguinal Folds. Face, scalp, palms of hands and soles of feet are rarely involved.
Si continua navegando, consideramos que acepta su uso. Systemic manifestations are progressive and may lead to serious complications: Etiology The etiopathogenesis of the disease remains unknown.